Thursday 16 August 2012

Type of Polycystic Kidney Disease


(1) polycystic kidney disease (PKD)
Polycystic kidney disease is a hereditary disease, showing the cortex and medulla of the kidney appeared in numerous sizes of the cysts, they have gradually grown up, squeezed in renal tissue, resulting in renal damage and renal dysfunction, when the renal clearance loss of function of the body of waste, due to the accumulation of toxins, the final form of uremia and life-threatening. Divided into autosomal dominant adult polycystic kidney disease (ADPKD) and autosomal recessive infantile polycystic kidney disease (ARPKD) are two types of polycystic kidney disease, according to their genetic characteristics.
(2) simple renal cysts (simpls renal cysts)
Simple renal cysts are the most common form of human renal disease, mainly seen in the adult aged over 50 is more common, simple renal cysts usually presents one side or one or a few cysts in both kidneys in general was isolated spherical, located in the renal cortex (also located in the deep cortex or medulla), and altered kidney shape.
3.Acquired renal cysts (ARCD)
Acquired renal cystic other than those due to renal disease (cystic kidney disease) caused by renal failure, renal cystic disease, on each side of renal cysts have more than one performance of multiple symmetry cyst " . More than 40% of the renal parenchyma by multiple cysts replaced by B ultrasound or CT can be found in more than four of the cyst.
(4) dysplasia, polycystic kidney disease (MCDK)
This disease is the most common neonatal abdominal mass, one of the reasons, the lesions often has the unilateral, segmental stenosis of the renal collecting system, bilateral often life-threatening. The majority of patients with prenatal ultrasound can be confirmed that the clinical manifestations of asymptomatic abdominal mass. Suffering from renal loss of normal shape, instead of the irregular size of the cyst, ipsilateral renal function, and is often accompanied by ureteral obstruction, the contralateral kidney compensatory hypertrophy, 10% of the contralateral input urinary obstruction.
5.Medullary sponge kidney (madullary sporge kidney):
Renal medullary sponge kidney is a common renal medullary cystic disease, one of. Is a relatively common renal abnormalities, the incidence rate of approximately 1/5000, the majority to 40 to 50 years old before onset. Which is characterized by medullary collecting duct cystic expansion to approximate the sponge from the gross appearance point of view, hence the name. Two kidney is normal or slightly enlarged, generally only the nipple area was the radioactive arranged), and hematuria and infection, a rare occurrence of uremia renal clusters of multiple stones
6.Renal medullary cystic disease (madullary cystic disease)
Renal medullary cystic disease and medullary sponge kidney, it is a rare hereditary nephropathy, 80% for recessive inheritance, 20% for the dominant inheritance. The common age of onset is in childhood, usually to young people the development of uremia, two kidney narrowing, multiple cysts in the medulla, with diameters ranging from 0.1 to 1 cm, tubular atrophy, 10% to 15% with retinitis pigmentosa.